Valine 50 Oral Supplement Unflavored 4 Gram Packet 30 Ct

What the brand says

Maple syrup urine disease is an inherited disorder of metabolism in which the enzyme necessary for the breakdown of amino acids lysine, leucine and isoleucine is lacking and the person has hyperreflexia (overactive reflexes) and urine with a characteristic maple syrup odor. Treatment includes a diet low in these amino acids. Valine50 amino acid medical food is for use in the dietary management of inborn errors of metabolism such as maple syrup urine disease, and to provide specific amounts of valine unable to be achieved by dietary modification alone. - Valine is an amino acid needed for growth in children and nitrogen balance in adults; Valine50 contains 1250 milligrams of L-Valine in a 4-gram packet.. Valine50 is or those as young as 1 year of age who have been diagnosed with certain metabolic disorders.. Valine50 can be mixed into other permitted food or drink such as a protein substitute.. Box contains 30 0.14-ounce packets of powdered amino acid medical food on a carbohydrate base..